CDH involves herniation of abdominal viscera into the thoracic cavity, causing severe ipsilateral and contralateral pulmonary hypoplasia and pulmonary hypertension.

Key Physiological Equations & Formulas

  • CDH Ventilation Goals (EURO-CDH Protocol): $$P_{insp} < 25\text{ cmH}_2\text{O}, \quad PEEP = 3-5\text{ cmH}_2\text{O}, \quad SpO_2 \ge 85-95\%, \quad PaCO_2 = 45-65\text{ mmHg}$$ Strict gentle ventilation to prevent barotrauma in hypoplastic lungs.

Practical Clinical Pearls & Bedside Rules

  • Avoid Bag-Mask Ventilation: Never bag-mask ventilate a suspected CDH infant in the delivery room; bag-masking distends the intrathoracic stomach and compresses the heart and lungs. Intubate immediately.
  • Nasogastric Decompression: Place large bore (8-10 Fr) double-lumen Replogle suction catheter to continuous low suction immediately at birth.

Initial Settings & Clinical Titration Protocol

ParameterRecommended Initial SettingTitration Goal / Safety Threshold
ModeConventional PC-CMV or HFOVStrictly limit peak inspiratory pressure (PIP <= 25 cmH2O).
ECMO IndicationsPre-ductal SpO2 < 85% or OI > 40 despite HFOV and iNOBridge to surgery and lung recovery.

Bedside Troubleshooting & Red Flags

Warning

Contralateral Pneumothorax: Iatrogenic rupture of the 'good' lung carries near 100% mortality. Maintain low peak pressures at all times.

Key Takeaways & Summary

  1. Always evaluate patient synchrony and physiological response before changing ventilator parameters.
  2. Maintain lung-protective strategies to minimize driving pressure ($\Delta P$) and mechanical power.
  3. Continuously reassess liberation and extubation readiness on daily morning rounds.